A case of congenital hepatic fibrosis without portal hypertension.
نویسندگان
چکیده
منابع مشابه
Congenital hepatic fibrosis in an aborted calf
An aborted female Holstein foetus with marked generalized anasarca was referred to the Excellence Centre for Ruminant Abortion and Neonatal Mortality, Ferdowsi University of Mashhad. On postmortem examination, red-tinged ascites, pale and firm liver with extreme irregularity and numerous round to oval slightly raised foci on the capsular surface were seen. Histological examination revealed wide...
متن کاملLaparoscopic distal splenoadrenal shunt for the treatment of portal hypertension in children with congenital hepatic fibrosis
BACKGROUND The distal splenorenal shunt is an effective procedure for the treatment of portal hypertension in children. However, there has been no report about laparoscopic distal splenorenal shunt in the treatment of portal hypertension in children. METHODS From December 2015 to August 2016, 4 children with upper gastrointestinal bleeding underwent laparoscopic distal splenoadrenal shunt. Po...
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Congenital Hepatic Fibrosis (CHF) is a rare disease that affects both the liver and kidneys. Congenital hepatic fibrosis (CHF) is an autosomal recessive inherited malformation defined pathologically by a variable degree of periportal fibrosis and irregularly shaped proliferating bile ducts. Affected individuals also have impaired renal function, usually caused, in children and teenagers, by an...
متن کاملSURGICAL EXPERIENCE WITH PORTAL HYPERTENSION DUE TO HEPATOPORTAL SCLEROSIS (NONCIRRHOTIC PORTAL FIBROSIS)
Hepatoportal sclerosis or idiopathic portal hypertension has a worldwide distribution with prevalence in developing and temperate countries. Of 64 patients with this disease seen during a twelve year period, 36 underwent splenectomy or a shunt procedure. The indications for surgical intervention were severe hypersplenism and persistent left upper abdominal pain andlorhistory of frequent ep...
متن کاملHepato-lienal fibrosis without cirrhosis: non-cirrhotic intrahepafic portal hypertension
In 1933, John McMichael was awarded a gold medal by the University of Edinburgh for his M.D. thesis. This was entitled 'The pathology of hepatolienal fibrosis' and was published in an abridged form in 1934 in the Journal of Pathology and Bacteriology. It was a masterly account of the pathological changes associated with portal hypertension. Pathological changes in spleen and portal vasculature ...
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ژورنال
عنوان ژورنال: Kanzo
سال: 1995
ISSN: 0451-4203,1881-3593
DOI: 10.2957/kanzo.36.101